Types of Budd-Chiari syndrome

Budd-Chiari syndrome is a relatively rare disorder caused by occlusion of hepatic veins. It presents with abdominal pain, ascites, and hepatomegally.

Budd-Chiari syndrome has four clinical variants:

  • acute
  • subacute
  • chronic
  • fulminant

Budd-Chiari syndrome can be:

  • primary (congenital obstruction  by webs or diaphragms)
  • secondary (multiple causes)

Budd-Chiari syndrome has three morphological types:

Type Description
Type I - truncal type occlusion of inferior vena cava with or without involvement of hepatic veins
Type II - radicular type occlusion of major hepatic veins
Type III - venooclusive type occlusion of small centrilobular veins


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