Types of Budd-Chiari syndrome

Budd-Chiari syndrome is a relatively rare disorder caused by occlusion of hepatic veins. It presents with abdominal pain, ascites, and hepatomegally.

Budd-Chiari syndrome has four clinical variants:

  • acute
  • subacute
  • chronic
  • fulminant

Budd-Chiari syndrome can be:

  • primary (congenital obstruction  by webs or diaphragms)
  • secondary (multiple causes)

Budd-Chiari syndrome has three morphological types:

Type Description
Type I - truncal type occlusion of inferior vena cava with or without involvement of hepatic veins
Type II - radicular type occlusion of major hepatic veins
Type III - venooclusive type occlusion of small centrilobular veins

References:

1. Malik T, Mehmood M, Rehman AU. Pakistan Armed Forces Medical Journal. 2009 Jun;3.
2. Langlet P, Escolano S, Valla D, Coste-Zeitoun D, Denie C, Mallet A, et al. Clinicopathological forms and prognostic index in Budd-Chiari syndrome. J. Hepatol. 2003 Oct;39(4):496–501.
3. Murphy FB, Steinberg HV, Shires GT 3rd, Martin LG, Bernardino ME. The Budd-Chiari syndrome: a review. AJR Am J Roentgenol. 1986 Jul;147(1):9–15.

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Updated 6/3/2015 12:56 by Lambert